Previously called cylindroma or adenocystic carcinoma, Adenoid cystic carcinoma (ACC) of the trachea is rare, it represents less than1%of all respiratory tract cancers. It is a slow-growing cancer, with pronlonged clinical course. Most patients present with dyspnea and wheeze/stridor, often mimic those of asthma. Surgical resection is the mainstay of treatment combined to adjuvant radiotherapy because of close resection margins.We report a case of primary ACC of trachea: a 45 years old female presented with dyspnea and stridor having this tracheal tumor treated by surgical resection and reconstruction with end to end anastomosis followed by adjuvant radiotherapy. At 6 months follow-up, our patient shows no evidence of disease with negative histological findings.
